Completely revised new edition of the premier reference on pediatric
liver disease. Liver Disease in Children, 3rd Edition provides
authoritative coverage of every aspect of liver disease affecting
infants, children, and adolescents. The book offers an integrated
approach to the science and clinical practice of pediatric hepatology
and charts the substantial progress in understanding and treating
these diseases. Chapters are written by international experts and
address the unique pathophysiology, manifestations, and management of
these disorders in the pediatric population. The third edition has
been thoroughly updated and features new contributions on liver
development, cholestatic and autoimmune disorders, fatty liver
disease, and inborn errors of metabolism. With the continued
evolution of pediatric hepatology as a discipline, this text remains
an essential reference for all physicians involved in the care of
children with liver disease.
? Third edition of the leading book on pediatric liver disease ?
Thoroughly updated with new chapters on liver development,
cholestatic and autoimmune disorders, fatty liver disease and inborn
errors of metabolism ? Provides a comprehensive, integrated approach
to the science and clinical practice of pediatric hepatology ?
Includes an eight page color insert with over ninety color photos
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Part I: 1. Embryology and development of the liver Ken Zaret; 2.
Functional development of the liver Saul J. Karpen and Frederick J.
Suchy; 3. Mechanisms of cholestasis Saul Karpen and Frederick J.
Suchy; 4. The cholangiopathies V. J. Desmet and Tania Roskams; 5.
Fulminant hepatic failure in children Peter F. Whitington and Philip
Squires; 6. Cirrhosis and chronic liver failure in children Ronald E.
Kleinman; 7. Portal hypertension Benjamin Shneider; 8. Laboratory
assessment of liver function and injury in children Vicky Ng; Part
II: 9. Approach to the infant with cholestasis Frederick Suchy; 10.
Medical and nutritional management of cholestasis Drew Feranchak and
Ronald J. Sokol; 11. Neonatal hepatitis and congenital infections
Philip Rosenthal; 12. Biliary atresia and other disorders of the
extrahepatic bile ducts Fred Ryckman, Jorge Bezerra and William
Balistreri; 13. Neonatal jaundice and disorders of bilirubin
metabolism Glenn R. Gourley; 14. Progressive familial intrahepatic
cholestasis Benjamin Shneider and Frederick Suchy; 15. Alagille
syndrome David Piccoli and Nancy Spinner; 16. Diseases of the
gallbladder James Heubi; Part III: 17. Acute and chronic viral
hepatitis William F. Balistreri; 18. Autoimmune hepatitis Giorgina
Meili-Vergani; 19. Sclerosing cholangitis William F. Balistreri; 20.
Drug and toxin-induced liver disease Eve Roberts; 21. Immune
deficiency and the liver Dino Hadzic; Part IV: 22. Laboratory
diagnosis of inborn errors of metabolism Piero Rinaldo; 23.
Alpha1antitrypsin deficiency David Perlmutter; 24. The liver and
biliary tract in cystic fibrosis Drew Frenanchak; 25. Inborn errors
of carbohydrate metabolism Fayez K. Ghishan; 26. Disorders of copper
metabolism Ronald J. Sokol; 27. Disorders of iron metabolism Michael
Narkewicz and Alex Knisely; 28. Porphyrins and porphyria Robert
Desnick; 29. Tyrosinemia Grant Mitchell; 30. The lysosomal storage
diseases Gregory Grabowski; 31. Disorders of bile acid metabolism
Kenneth Setchell; 32. Inborn errors of fatty acid oxidation Jamal
Ibdah; 33. Mitochondrial hepatopathies Ronald Sokol; 34. Non-
alcoholic fatty liver disease Jeffrey Swimmer; 35. Perioxisomal
disorders Paul Watkins and Kathleen Schwartz; 36. Disorders of the
urea cycle Mark Batshaw and Mendel Tuchman; Part V: 37. Bacterial,
parasitic and fungal infections of the liver Donald Novak; 38.
Systemic disease and the liver John Bucuvalas and Michael K. Farrell;
39. Fibrocystic liver disease Maureen Jonas and Antonio Perez-Atayde;
40. Hepatic tumors in child