Arrhythmogenic right ventricular cardiomyopathy/dysplasia

This book covers all aspects (biological, pathological, genetic,
clinical and therapeutical) of arrhythmogenic right ventricular
cardiomyopathy/dysplasia, a recent cardiomyopathy which represents a
very high risk of sudden death in the young and in athletes. The
monograph presents the results of 5-year research program on ARVC/D
supported by grants of both the European Commission and the NIH,
which enabled the discovery of seven disease-causing genes, thus
opening new avenues for the early identification of affected patients
and for sudden death prevention.

A panel of top scientists, both European and Americans, contributed
to this volume, which will be an essential reference for
professionals and residents in cardiology, radiology, human genetics,
and sport medicine.

차 례
Introduction.- Advances in genetics: dominant forms.- Advances in
genetics: recessive forms.- Genetically modified animal models.-
Genotype-phenotype correlations.- ARVC/D in spontaneous animal
models.- Endomyocardial biopsy and autopsy features.- Cell adhesion
pathology.- Ultrastructural substrates.- Possible or contributing
role of viruses.- Diagnosis of ARVC/D: Task Force Criteria including
modifications for family members.- Strengths and weaknesses of the
Task Force Criteria: proposed modifications.- ARVC/D versus right
ventricular outflow tract tachycardia.- ECG and signal average ECG.-
Echocardiography.- MR and CT imaging.- Angiocardiography.-
Electrophysiologic study including voltage mapping.- Antiarrhythmic
drug therapy and risk stratification.- Catheter ablation.-
Implantable cardioverter defibrillator.- Management of heart failure.-
Sudden death in athletes.