Liver Disease in Children-2판(2002)

Summary:
This is the definitive book on pediatric liver disease,
providing extensive, well-edited information that is not easily
accessible or available in other textbooks. The book contains
comprehensive information that explains the pathophysiology,
clinical and laboratory diagnosis and clinical manifestations of
liver disease. This is a "must have" for those interested in
this rapidly growing pediatric subspeciality.

Table of Contents
Contributing Authors
Preface to the First Edition
Preface
Sect. I Pathophysiology of Pediatric Liver Disease 1
1 Structural and Functional Development of the Liver 3
2 Mechanisms and Morphology of Cholestasis 23
3 The Cholangiopathies 39
4 Fulminant Hepatic Failure in Children 63
5 Cirrhosis and Chronic Liver Failure 89
6 Portal Hypertension 129
Sect.II Evaluation of Liver Disease 153
7 Laboratory Assessment of Liver Function and Injury in Children 155
8 Laboratory Diagnosis of Inborn Errors of Metabolism 171
Sect. III Cholestatic Liver Diseases 185
9 Approach to the Infant with Cholestasis 187
10 Medical and Nutritional Management of Cholestasis 195
11 Neonatal Hepatitis and Congenital Infections 239
12 Biliary Atresia and Other Disorders of the Extrahepatic Bile Ducts 253
13 Neonatal Jaundice and Disorders of Bilirubin Metabolism 275
14 Familial Hepatocellular Cholestasis 315
15 Alagille Syndrome 327
16 Diseases of the Gallbladder in Infancy, Childhood, and Adolescence 343
Sect. IV Hepatitis and Immune Disorders 363
17 Acute and Chronic Viral Hepatitis 365
18 Autoimmune Hepatitis 429
19 Sclerosing Cholangitis 443
20 Drug-Induced Liver Disease 463
21 Immune Deficiency and Liver Disease 493
Sect. V Metabolic Liver Disease 503
22 Approach to the Child with Metabolic Liver Disease 505
23 [alpha][subscript 1]-Antitrypsin Deficiency 523
24 The Liver and Biliary Tract in Cystic Fibrosis 549
25 Inborn Errors of Carbohydrate Metabolism 565
26 Copper and Iron Storage Disorders 595
27 Neonatal Hemochromatosis 641
28 Porphyrins and Prophyria 649
29 Tyrosinemia 667
30 The Lysosomal Storage Diseases 687
31 Disorders of Bile Acid Synthesis and Metabolism: A Metabolic Basis for Liver
Disease 701
32 Inborn Defects in Mitochondrial Fatty Acid Oxidation 735
33 Mitochondrial Hepatopathies 787
34 Peroxisomal Diseases 811
35 Disorders of the Urea Cycle 827
Sect. VI Other Conditions and Issues in Pediatric Hepatology 843
36 Bacterial, Parasitic, and Fungal Infections of the Liver 845
37 Systemic Disease and the Liver 869
38 Fibrocystic Liver Disease 899
39 Hepatic Tumors in Children 915
40 Liver Transplantation in Children 949
Subject Index 975